Aravena, Carlos Labarca, Gonzalo Venegas, Carmen Arenas, Alex Rada, Gabriel Comparison 4. <p>Acute exacerbation.</p> systematic review;rr;literature search;mortality;function tests;quality assessment;fvc;5 RCTs;ipf;data extraction;benefit;findings table;decades pirfenidone;pirfenidone treatment;exacerbation;Idiopathic Pulmonary Fibrosis;collagen production;decline progression;outcome;ic;GRADE approach;pfs;language restriction 2015-08-26
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10.1371/journal.pone.0136160.g006